Podcast
Questions and Answers
What is the purpose of L-arginine supplementation in UCD patients?
What is the purpose of L-arginine supplementation in UCD patients?
- To stimulate appetite
- To increase ammonia production
- To prevent protein catabolism
- To prevent arginine deficiency and assist in waste nitrogen excretion (correct)
What is the maximum percentage of total kcal that CHO should not exceed in a low-protein diet for UCD patients?
What is the maximum percentage of total kcal that CHO should not exceed in a low-protein diet for UCD patients?
- 50% (correct)
- 40%
- 60%
- 30%
What is the frequency of monitoring plasma ammonia levels in UCD patients initially?
What is the frequency of monitoring plasma ammonia levels in UCD patients initially?
- Weekly
- Monthly
- Quarterly
- Daily (correct)
What is the purpose of sodium benzoate in UCD patients?
What is the purpose of sodium benzoate in UCD patients?
What is the recommended dietary intake of protein for UCD patients?
What is the recommended dietary intake of protein for UCD patients?
What is the purpose of measuring plasma albumin and globulin levels in UCD patients?
What is the purpose of measuring plasma albumin and globulin levels in UCD patients?
What is the goal of prescribing sodium benzoate, sodium phenylacetate, or sodium phenylbutyrate in the management of UCD?
What is the goal of prescribing sodium benzoate, sodium phenylacetate, or sodium phenylbutyrate in the management of UCD?
What is the role of L-arginine or L-citrulline supplementation in UCD management?
What is the role of L-arginine or L-citrulline supplementation in UCD management?
What is the target range for plasma ammonia levels in UCD management?
What is the target range for plasma ammonia levels in UCD management?
Why is protein restriction based on serum ammonia levels in UCD management?
Why is protein restriction based on serum ammonia levels in UCD management?
What is the purpose of using an EAA mixture in UCD nutrition therapy?
What is the purpose of using an EAA mixture in UCD nutrition therapy?
What is the diagnostic significance of measuring plasma ammonia levels in UCD?
What is the diagnostic significance of measuring plasma ammonia levels in UCD?
What is the primary function of the urea cycle in the body?
What is the primary function of the urea cycle in the body?
What is the consequence of a deficiency in N-acetylglutamate synthetase (NAGS) in the urea cycle?
What is the consequence of a deficiency in N-acetylglutamate synthetase (NAGS) in the urea cycle?
What is the primary mode of inheritance for urea cycle disorders (UCDs)?
What is the primary mode of inheritance for urea cycle disorders (UCDs)?
What is the main clinical presentation of urea cycle disorders (UCDs)?
What is the main clinical presentation of urea cycle disorders (UCDs)?
Which of the following is NOT a factor that influences the degree of hyperammonemia in urea cycle disorders (UCDs)?
Which of the following is NOT a factor that influences the degree of hyperammonemia in urea cycle disorders (UCDs)?
What is the typical location where the urea cycle operates?
What is the typical location where the urea cycle operates?
