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1.Tics, are; A. Stereotyped' motor behaviors. B. Unlike stereotypies less predictable and often last only a few seconds or less (although they can occur repeatedly, in clusters or in longer patterns) C. 'wax and wane' and change over time. D. More common under circumstances of stress...

1.Tics, are; A. Stereotyped' motor behaviors. B. Unlike stereotypies less predictable and often last only a few seconds or less (although they can occur repeatedly, in clusters or in longer patterns) C. 'wax and wane' and change over time. D. More common under circumstances of stress, anger, excitement, or anxiety E. None of them F. All above 2\. Tourette syndrome criteria met all, except one: A. Both vocal and motor, complex tics B. Comorbid conditions C. Lasts less than 1 year D. None of above E. All above 3\. When Tics are the main problem, in Tourette syndrome, first line therapy include: A. Clonidine initially; When clonidine is ineffective or not well tolerated, haloperidol and Pimozide can be used. B. Stimulant medication C. SSRI antidepressants D. Levodopa 4\. In Hemiplegic cerebral palsy we can see all, except one: A. Tiptoe walking. B. Muscle hypotonia C. C Ankle clonus and Babinski sign E. The deep tendon reflexes are increased, F. Weakness of the hand and foot dorsiflexors present G. Equinovarus deformity of the foot 5\. Several drugs can be used to treat spasticity, including all, except one; D. Levodopa E. Oral diazepam, F. Baclofen H. Dantrolene 6\. A person with adhd- predominantly which type, has a hard time" putting on the brakes" before acting (choose the right word) A. Hyperactivity -- impulsivity B. Attention deficit C. Oppositional disorder 7\. Children with ADHD often have a smaller: A. Total brain B. Spinal cord C. Frontal lobe cortex D. Occipital lobe cortex 8\. By what age is autism usually diagnosed: A. Age 12-16 months B. Age 2-2.5 y C. Age 18 months D. Age 3-4 y 9\. Which of the following is a sign of autism: A. 2 years old child does not react or respond when the name is called B. Child consistently does not seem interested in the reactions of others, especially the reactions of parents C. Person does not seem aware of feelings of others D. All of the above 10\. Which of the following causes autism: A. Cold parenting B. Poor prenatal nutrition C. A single gene or chromosome 21 A. There is no known A. Childhood disintegrative disorder B. Aspergers syndrome C. Typical autism D. REtt s disorder E. Mental retardation. A. Spastic paralysis B. Flaccid paralysis C. Mixed: Both symptoms: upper and lower motor lesions D. D\) Myashetnia gravis A. Gbs: inflammatory acquired poluneuropathy- B. ) diabetihic polyneurolopathy C. Congenital sensory motor polyeuiropathies D Myashetnia gravis 14\. Rapid fatigue of muscles, with progressive worsening over the day or with repetitive activity, is typical for: A. GBS B. Multiple sclerosis C. Myasthenia gravis D. Diabetic polyneuropathy 15\. Duchenne muscular dystrophy is: A. Autosomal dominant disorder B. Autosomal recessive disorder C. An X-linked disorder 16\. In Duchenne muscular dystrophy patient have: A. Spastic gait B. Shuffling gait C. Steppage gait D. Waddling gait 17\. In the case of Myasthenia Gravis we see on enmg: a. Eldecrement on 3 hc repetitive stimulation b. Myotonic phenomena (myotonic discharges with specific sounds) c. Motor action amplitude decreased 18\. All these are generalized episeizures except one: A. Absence seizures B. Myoclonic absences C. Infantile spasms D. Atonic seizures (atonic falls) E. BRE, with orofacial spasms and guttural sounds 19\. The characteristic electroencephalographic (EEG) patterns of typical absences consist of: A. Generalized 3-Hz spike-and-wave activity. B. Generalized 2-2.5-Hz spike-and-wave activity. C. Generalized poly spike and wave activity D. Focal delta activity in fronto temporal areas 20\. The first-choice therapy of Childhood absence epilepsy is: A. Valproic acid B. Ethosuximide C. Carbamazepine E. Topamax F. Lamotrigine G. Phenobarbital 21\. A subset of patients, with Childhood absence epilepsy, also has generalized tonic-clonic seizures, for these children, the first choice therapy, to prevent both absence and convulsive seizures, is: D. Valproic acid E. Ethosuximide F. Carbamazepine G. Topamax H. Lamotrigine I. Phenobarbital 22\. In Benign Rolandic epilepsy, Affected children usually have: A. Focal motor seizures involving: the face and arm (abnormal movement or sensation around the face and mouth, drooling, rhythmic guttural sound) I B. Myoclonic jerks C. Typical abscense seizures D. Atonic falls E. Infantile spasms 23\. Infantile spasms are: A. Atonic falls B. Brief contractions of the neck, trunk, and arm muscles, followed by a phase of sustained Muscle contraction lasting less than 2 seconds C. Myoclonic jerks D. Staring with eyelid myoclonus 24\. Hypsarrhythmia consists of: A. Generalized 3-Hz spike-and-wave activity. B. Generalized 2-2.5-Hz spike-and-wave activity. C. Chaotic high-voltage slow waves, spikes, and multifocal spikes D. Diffuse fast beta 25\. Patients, with Idiopathic intracranial hypertension (pseudotumor cerebri), exhibit all symptoms, except one: A. A daily debilitating headache B. Associated with diplopia, C. Abducens palsy, D. Hearing loss E. Transient visual obscurations, F. Papilledema. 26\. A 7-year-old girl with history of muscle jerks in the early morning, or with sleep deprivation, presents with a generalized tonic clonic jerks after a late night playing video games. Which of the following is the most likely diagnosis? A. Juvenile myoclonic epilepsy B. Rolandic epilepsy C. West syndrome D. Landau-kleffner syndrome 27\. A 24-year-old female is diagnosed with a complex partial seizure disorder. Which of the following would be typical automatisms that can occur in complex partial seizures? A. Lip smacking, chewing, gesturing B. Singing and coughing C. Chorelform dance-like movements D. Rigid arm motions directed laterally 28\. A 9-year-old boy is diagnosed with absence seizures. Which of the following would most likely best describes his seizure episodes? A. Tremulousness of the right arm in the absence of other movement disorder B. Momentary lapses in awareness, accompanied by motionless staring and cessation of any ongoing activity C. Alternate flexion and extension and rigidity of the arms and legs D. Sudden loss of posture and falling unconscious to the floor 29\. A 8-year-old boy presents with right-sided neck pain and left-sided numbness of face, arm, and leg after a chiropractic manipulation of his neck. Choose the most appropriate diagnosis from the following list: A. Subarachnoid headache B. Sinusitis C. Post-LP headache D. Carotid dissection E. Pseudotumor cerebri F. Migraine with aura G. Migraine without aura 30\. A 7-year-old girl presents with nasal congestion and post-nasal drip, complaining of bilateral pain above and around her eyes. Choose the most appropriate diagnosis from the following list: A. Subarachnoid headache B. Sinusitis C. Post-LP headache D. Carotid dissection E. Pseudotumor cerebri F. Migraine with aura G. Migraine without aura 31\. 16-year-old college student studying for final examinations complains of recurrent right temple pain, preceded by flashing lights, and followed by nausea lasting 3-5 hours. Choose the most appropriate diagnosis from the following list: A. Subarachnoid headache B. Sinusitis C. Post-LP headache D. Carotid dissection E. Pseudotumor cerebri F. Migraine with aura G. Migraine without aura 32\. The adults, of neurofibromatosis type 1, present all, except one: A. Six or more café-au-lait spots larger than 5 mm B. Lisch nodules. C. Neurofibromas D. Syringobulbia E. Optic gliomas 33\. NF2 (neurofibromatosis, type 2)predisposes patients to multiple intracranial and spinal tumors, including all, except one: A. Bilateral acoustic schwannomas, B. Schwannomas of other cranial and spinal nerves, C. Hemangiomas D. Meningiomas, E. Gliomas 34\. Tuberous sclerosis skin lesions are all, except one; A. Café au lait spots B. Hypomelanotic macules (ash leaf spots). C. Facial angiofibromas (adenoma sebaceum) D. Shagreen patches, elevated, rough plaques 35\. Sturge-Weber syndrome is associated with one: A. Café au lait spots B. Hypomelanotic macules (ash leaf spots). C. Facial angiofibromas (adenoma sebaceum) D. Shagreen patches, elevated, rough plaques E. Ipsilateral facial port-wine stain 36\. Periventricular deep white matter signal change, in particular around the atria and frontal horns with sparing of subcortical U fibers, leading to a "butterfly pattern", is characteristic to: A. Neurofibromatosis type 1 B. Neurofibromatosis type 2 C. Sturge-Weber syndrome D. Metachromatic leukodystrophy (MLD) 37\. In a meningocele, wee see: A. The skin of the back is apparently intact, but defects of the underlying bone or spinal canal are present B. The spinal canal and cystic meninges are exposed on the back, but the underlying spinal cord is anatomically and functionally intact. C. All spinal cord structures are exposed on back 38\. Dandy-Walker malformation is diagnosed on the basis of: A. Complete or partial agenesis of the cerebellar vermis, B. Cystic dilation of the fourth ventricle, C. And enlarged posterior fossa D. None of them all of them E. All of them 39\. Macrocrania is: A. Enlargement of the ventricles; B. Increased skull thickness C. Enlargement of the brain. 40\. Lissencephaly represents: A. Varying degrees of failure of the forebrain (prosencephalon) to divide into two distinct cerebral hemispheres. B. By clefts within the cerebral hemispheres that extend from the cortical surface to the ventricular cavity. C. A severe defect in cortical migration results in a smooth brain without sulcation (agyria)