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Questions and Answers
What is the primary purpose of aortic valvotomy?
What is the primary purpose of aortic valvotomy?
What condition is characterized by localized narrowing of the aorta?
What condition is characterized by localized narrowing of the aorta?
What happens to pressure in the right side of the heart during defects with decreased pulmonary blood flow?
What happens to pressure in the right side of the heart during defects with decreased pulmonary blood flow?
Which of the following is a pathognomonic sign of coarctation of the aorta?
Which of the following is a pathognomonic sign of coarctation of the aorta?
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In Tetralogy of Fallot, which defect is NOT one of the four components?
In Tetralogy of Fallot, which defect is NOT one of the four components?
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What is the primary effect of decreased pulmonary blood flow in cyanotic heart defects?
What is the primary effect of decreased pulmonary blood flow in cyanotic heart defects?
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Which of the following symptoms is typically observed in cases of coarctation of the aorta?
Which of the following symptoms is typically observed in cases of coarctation of the aorta?
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What is the clinical implication of rapid and bounding pulses found in coarctation of the aorta?
What is the clinical implication of rapid and bounding pulses found in coarctation of the aorta?
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What is one of the complications that can arise due to the growth of the uterus during pregnancy?
What is one of the complications that can arise due to the growth of the uterus during pregnancy?
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Which of the following is a clinical manifestation of chronic venous insufficiency?
Which of the following is a clinical manifestation of chronic venous insufficiency?
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What role does compression therapy play in managing potential pregnancy complications?
What role does compression therapy play in managing potential pregnancy complications?
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What area is notably affected by venous stasis resulting from reflux of venous blood?
What area is notably affected by venous stasis resulting from reflux of venous blood?
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What is a recommended position to alleviate symptoms during pregnancy?
What is a recommended position to alleviate symptoms during pregnancy?
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What is the primary goal of surgical repair for ASD 3?
What is the primary goal of surgical repair for ASD 3?
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What condition is characterized by an abnormal opening between the right and left ventricles?
What condition is characterized by an abnormal opening between the right and left ventricles?
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What is a common symptom of large VSDs?
What is a common symptom of large VSDs?
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What medical treatment stimulates the muscles inside the PDA to constrict?
What medical treatment stimulates the muscles inside the PDA to constrict?
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What type of defect is characterized by narrowing or stricture of the aortic valve?
What type of defect is characterized by narrowing or stricture of the aortic valve?
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What is the palliative treatment option for infants with severe symptoms due to ASD 3?
What is the palliative treatment option for infants with severe symptoms due to ASD 3?
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What is a significant risk factor for developing PDA?
What is a significant risk factor for developing PDA?
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What is an indicator of pulmonary stenosis?
What is an indicator of pulmonary stenosis?
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What is a common non-surgical management technique for obstructive defects?
What is a common non-surgical management technique for obstructive defects?
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What is the extreme form of pulmonary stenosis where there is no blood flow to the lungs?
What is the extreme form of pulmonary stenosis where there is no blood flow to the lungs?
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What is the main complication of supracardiac TAPVR?
What is the main complication of supracardiac TAPVR?
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Which assessment finding is commonly associated with infracardiac TAPVR?
Which assessment finding is commonly associated with infracardiac TAPVR?
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What surgical procedure is performed in treating TAPVR?
What surgical procedure is performed in treating TAPVR?
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Which of the following is a common clinical manifestation of venous thromboembolism?
Which of the following is a common clinical manifestation of venous thromboembolism?
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What is the primary goal of medical management for venous thromboembolism?
What is the primary goal of medical management for venous thromboembolism?
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Which factor does NOT contribute to Virchow’s triad?
Which factor does NOT contribute to Virchow’s triad?
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What is a common risk factor for venous thromboembolism?
What is a common risk factor for venous thromboembolism?
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Which prevention measure is effective for reducing the risk of DVT?
Which prevention measure is effective for reducing the risk of DVT?
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What is the significance of Homan Sign in diagnosing DVT?
What is the significance of Homan Sign in diagnosing DVT?
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What symptom might indicate deep vein thrombosis rather than superficial vein issues?
What symptom might indicate deep vein thrombosis rather than superficial vein issues?
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What is the primary characteristic of Primary Polycythemia or Polycythemia vera?
What is the primary characteristic of Primary Polycythemia or Polycythemia vera?
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Which of the following symptoms is associated with secondary polycythemia?
Which of the following symptoms is associated with secondary polycythemia?
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What treatment is typically used to manage Primary Polycythemia vera?
What treatment is typically used to manage Primary Polycythemia vera?
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In Secondary Polycythemia, what is a common cause of increased erythropoietin production?
In Secondary Polycythemia, what is a common cause of increased erythropoietin production?
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What is the main complication associated with Primary Polycythemia vera?
What is the main complication associated with Primary Polycythemia vera?
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What is a key laboratory finding in diagnosing Primary Polycythemia vera?
What is a key laboratory finding in diagnosing Primary Polycythemia vera?
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What is the recommended management for symptomatic patients with elevated red blood cell counts?
What is the recommended management for symptomatic patients with elevated red blood cell counts?
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Which condition is least likely linked to the symptoms of Primary Polycythemia vera?
Which condition is least likely linked to the symptoms of Primary Polycythemia vera?
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Which management strategy is prioritized for Secondary Polycythemia?
Which management strategy is prioritized for Secondary Polycythemia?
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Which of the following conditions is NOT commonly associated with Primary Polycythemia vera?
Which of the following conditions is NOT commonly associated with Primary Polycythemia vera?
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Study Notes
Sinus Venosus Defect (ASD 3)
- Opening near the junction of the superior vena cava
- May be asymptomatic or present with respiratory tract infections, dyspnea on exertion, and congestive heart failure
- May experience feeding difficulties
- Management options include cardiac catheterization or open heart surgery
- Surgical repair aims to reduce excessive pulmonary blood flow and protect pulmonary vasculature from hypertrophy and irreversible pulmonary hypertension
Ventricular Septal Defect (VSD)
- Abnormal opening between the right and left ventricles
- Small VSDs are usually asymptomatic and often close spontaneously during the first year of life
- Large VSDs can lead to congestive heart failure (CHF) with symptoms like tachypnea, tachycardia, excessive sweating, hepatomegaly, frequent upper respiratory infections, poor weight gain, failure to thrive, feeding difficulties, and decreased exercise tolerance
Patent Ductus Arteriosus (PDA)
- Failure of the fetal ductus arteriosus to close within the first weeks of life
- High risk factors include maternal rubella exposure during pregnancy
- Assessment includes a machinery-like murmur, asymptomatic presentation, and signs and symptoms of CHF and decreased cardiac output
- Management options include medical treatment with Indomethacin (Indocin) and surgical ligation
Obstructive Defects
- Blockage of blood flow in the heart due to narrowing (stenosis)
- Can result in decreased cardiac output, ventricular hypertrophy, and pulmonary vascular congestion
Aortic Stenosis
- Narrowing of the aortic valve causes resistance to blood flow in the left ventricle
- Assessment findings include a characteristic murmur and signs of decreased cardiac output in infants and exercise intolerance, chest pain, and dizziness when standing for long periods in children
- Treatment includes minimally invasive procedures like aortic valvotomy or valvuloplasty, and valve replacement
Coarctation of the Aorta
- Localized narrowing of the aorta
- Assessment includes absent femoral pulses, higher blood pressure in the upper extremities, and weaker or absent pulses in the lower extremities
- Management options include balloon angioplasty and surgical resection with end-to-end anastomosis of the aorta
Pulmonary Stenosis
- Narrowing at the entrance to the pulmonary artery causing resistance to blood flow
- Leads to right ventricular hypertrophy and decreased pulmonary blood flow
- Pulmonary atresia is the extreme form with total fusion of the commissures and no blood flow to the lungs
- Treatment includes balloon valvuloplasty and surgical valvotomy
Tetralogy of Fallot
- Four defects: pulmonary stenosis, VSD, overriding aorta, and supracardiac total anomalous pulmonary venous return (TAPVR)
- Assessment involves a characteristic murmur, moderate to severe CHF, variable cyanosis, poor growth, and activity intolerance
- Surgical treatment aims to close the VSD, implant a conduit and valve to connect the right ventricle with the pulmonary artery, and construct a single large vessel and aorta
TAPVR (Total Anomalous Pulmonary Venous Return)
- Pulmonary veins drain into the right atrium instead of the left
- Classified based on location: Supracardiac, Infracardiac, and Cardiac
- Blood mixes in the common great artery causing desaturation and hypoxemia
- Surgical treatment aims to create a connection between the pulmonary veins and the left atrium
Venous Thromboembolism (VTE)
- Deep vein thrombosis (DVT) and pulmonary embolism
- Often clinically silent and frequently underdiagnosed
- Risk factors include endothelial damage, venous stasis, and altered coagulation
- Pathophysiology follows Virchow's triad: endothelial damage, venous stasis, and altered coagulation
- Deep veins may show edema, warmth, and prominence, while superficial veins may present with tenderness, redness, and warmth
- Diagnostic exams include careful assessment of lower extremities and Homan's sign (although not entirely reliable)
- Prevention measures include identification of risk factors, compression stockings and devices, early ambulation, leg exercises, low molecular weight heparin (LMWH), and lifestyle changes
- Medical management aims to prevent thrombus growth and fragmentation
- Nursing management includes monitoring for complications, providing comfort, and encouraging exercise
Polycythemia
- Classified as primary (Polycythemia Vera) or secondary
- Primary Polycythemia Vera is due to a mutation leading to overproduction of red blood cells
- Secondary Polycythemia occurs due to factors reducing oxygen reaching tissues, like smoking, high altitude, or congenital heart disease
- Diagnosis includes elevated hemoglobin, positive JAK2 gene, and decreased serum erythropoietin
- Clinical manifestations include ruddy complexion, splenomegaly, and symptoms from increased blood volume
- Medical management for Primary Polycythemia Vera focuses on reducing risk of thrombosis and bleeding, and treating contributing factors
- Medical management for Secondary Polycythemia involves treating the underlying condition and therapeutic phlebotomy
Hemophilia
- Group of bleeding disorders due to deficiency of specific coagulation proteins
- Most common types include Hemophilia A and Hemophilia B
- Characterized by excessive bleeding and prolonged clotting time
- Treatment involves replacement therapy with missing coagulation factor
- Management includes careful monitoring of blood coagulation factors and preventing bleeding episodes
Vascular Disorders
- Include conditions affecting blood vessels, such as venous thromboembolism and polycythemia
- Management focuses on addressing specific causes and complications
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Description
Explore the characteristics and management of common cardiac defects including Atrial Septal Defect (ASD), Ventricular Septal Defect (VSD), and Patent Ductus Arteriosus (PDA). Understand their symptoms, potential complications, and treatment options to enhance your knowledge in pediatric cardiology.