Podcast
Questions and Answers
Where does the first reaction of the urea cycle take place?
Where does the first reaction of the urea cycle take place?
- Golgi apparatus
- Mitochondria (correct)
- Endoplasmic reticulum
- Cytosol
What is the activator of Carbamoyl phosphate synthetase I (CPS I)?
What is the activator of Carbamoyl phosphate synthetase I (CPS I)?
- N-Acetyl-Glutamate (correct)
- Carbamoyl phosphate
- Ornithine
- Argininosuccinate
Which syndrome is caused by the mutation of the ornithine transport gene?
Which syndrome is caused by the mutation of the ornithine transport gene?
- Huntington's disease
- HHH syndrome (correct)
- Marfan syndrome
- Turner syndrome
What is the product formed when citrulline reacts with 1 more ammonia from Aspartic acid in the cytosol?
What is the product formed when citrulline reacts with 1 more ammonia from Aspartic acid in the cytosol?
Why do we still need to get ornithine from the diet if it is immediately converted to urea?
Why do we still need to get ornithine from the diet if it is immediately converted to urea?
Which enzyme catalyzes the conversion of arginine to urea and ornithine in the urea cycle?
Which enzyme catalyzes the conversion of arginine to urea and ornithine in the urea cycle?
What is the immediate consequence of the deficiency of any enzyme in the urea cycle?
What is the immediate consequence of the deficiency of any enzyme in the urea cycle?
Which step in the urea cycle involves the detoxification of 1 mole of ammonia?
Which step in the urea cycle involves the detoxification of 1 mole of ammonia?
Which molecule is NOT produced as a direct result of the urea cycle?
Which molecule is NOT produced as a direct result of the urea cycle?
What is the total amount of ATP consumed in both the 1st and 3rd reactions of the urea cycle?
What is the total amount of ATP consumed in both the 1st and 3rd reactions of the urea cycle?
