Podcast
Questions and Answers
Which of the following is a characteristic feature of idiopathic pleuroparenchymal fibroelastosis (PPFE)?
Which of the following is a characteristic feature of idiopathic pleuroparenchymal fibroelastosis (PPFE)?
- Elevated urinary level of desmosines
- Elevated serum level of latent transforming growth factor-beta binding protein 4
- Elevated serum level of surfactant protein-D (correct)
- Elevated serum level of Krebs von den Lungen-6
Which imaging technique is commonly used to assess upper-lobe lung volume in idiopathic pleuroparenchymal fibroelastosis (PPFE)?
Which imaging technique is commonly used to assess upper-lobe lung volume in idiopathic pleuroparenchymal fibroelastosis (PPFE)?
- Magnetic resonance imaging (MRI)
- Three-dimensional computed tomography (CT) (correct)
- Positron emission tomography (PET)
- Ultrasound
Which biomarker has been proposed as a noninvasive diagnostic tool for idiopathic pleuroparenchymal fibroelastosis (PPFE)?
Which biomarker has been proposed as a noninvasive diagnostic tool for idiopathic pleuroparenchymal fibroelastosis (PPFE)?
- Serum Krebs von den Lungen-6
- Urinary desmosines (correct)
- Serum surfactant protein-D
- Serum latent transforming growth factor-beta binding protein 4
Which gene mutation has been associated with pleuroparenchymal fibroelastosis (PPFE)?
Which gene mutation has been associated with pleuroparenchymal fibroelastosis (PPFE)?
Which treatment option has limited efficacy for idiopathic pleuroparenchymal fibroelastosis (PPFE)?
Which treatment option has limited efficacy for idiopathic pleuroparenchymal fibroelastosis (PPFE)?