Lactic Acidosis 1 Multienzyme Complexes

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18 Questions

Qual es le avantages de complexos multi enzimatic de acidos lactic?

Protection contra reactiones lateral

Quales es membros del familia del complexo de dehydrogenase de acido α-keto?

Pyruvate dehydrogenase complex

Qual es le cofactor necessari pro dihydrolipoyl transacylase in le complexo keto acid dehydrogenase?

Acido lipoic

Qual es le function de E3 in le complexo keto acid dehydrogenase?

Reduction del substrato

Qual es le vita vitae necessari pro l'enzyma E2 in le complexo pyruvate dehydrogenase?

B5

Quale enzima forma parte del familia del complexo α-keto acid dehydrogenase?

α-keto acid dehydrogenase (E1)

Qual es le effetto del ATP, NADH e Acetyl CoA in le covalente phosphorilation?

Inhibition

Qual es le activator allosteric del kinase in le regulation complex 7 8?

ATP

Quales es le activatores allosteric del phosphatase?

AMP

Que representa le mutation del subunitate E1 o E2 del complexo de pyruvate dehydrogenase?

Deficientia hereditari

Qual es le consequentias del piling de acetyl CoA o acyl CoA in le corpore?

Inhibition de glycolysis

Qual es le function del cytosol in le production de lactate?

Conversion de glucose a lactate

Qual es le subunitate dehydrogenase de dihydrolipoil?

E3

Qual es un possibile defecto hereditari del complexo dehydrogenase de piruvato?

Mutacion del subunitate E1

In le caso reportate, qual es le concentration de lactate in le sanguine del infante de 8 menses?

9 mM

Quod representa un possibile symptomate clinic in babies con defectos in le complexo dehydrogenase de piruvato?

Incapacitate de ganar peso

Qual es le cofactor que lipoic acid require pro functionar efficacemente?

Acido pantotenico (B5)

Quid representa un possibile consequentia del piling de acetyl CoA o acyl CoA pro le cellulas?

Accumulation de toxinas cellular

Explore the advantages of multienzyme complexes in lactic acidosis, including minimal diffusion, time factor, protection for intermediates, and more. Learn about the common regulation and different complexes like α-keto acid dehydrogenase complex family and pyruvate dehydrogenase complex.

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