Lactic Acidosis 1 Multienzyme Complexes

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Questions and Answers

Qual es le avantages de complexos multi enzimatic de acidos lactic?

  • Tempo protection
  • Protection contra reactiones lateral (correct)
  • Regulation commun
  • Diffusion minimal

Quales es membros del familia del complexo de dehydrogenase de acido α-keto?

  • Pyruvate dehydrogenase complex (correct)
  • Lipid synthesis complex
  • Citric acid cycle complex
  • Gluconeogenesis complex

Qual es le cofactor necessari pro dihydrolipoyl transacylase in le complexo keto acid dehydrogenase?

  • Vitamina D
  • Vitamina A
  • Acido lipoic (correct)
  • Vitamina C

Qual es le function de E3 in le complexo keto acid dehydrogenase?

<p>Reduction del substrato (C)</p> Signup and view all the answers

Qual es le vita vitae necessari pro l'enzyma E2 in le complexo pyruvate dehydrogenase?

<p>B5 (C)</p> Signup and view all the answers

Quale enzima forma parte del familia del complexo α-keto acid dehydrogenase?

<p>α-keto acid dehydrogenase (E1) (D)</p> Signup and view all the answers

Qual es le effetto del ATP, NADH e Acetyl CoA in le covalente phosphorilation?

<p>Inhibition (A)</p> Signup and view all the answers

Qual es le activator allosteric del kinase in le regulation complex 7 8?

<p>ATP (B)</p> Signup and view all the answers

Quales es le activatores allosteric del phosphatase?

<p>AMP (A)</p> Signup and view all the answers

Que representa le mutation del subunitate E1 o E2 del complexo de pyruvate dehydrogenase?

<p>Deficientia hereditari (B)</p> Signup and view all the answers

Qual es le consequentias del piling de acetyl CoA o acyl CoA in le corpore?

<p>Inhibition de glycolysis (A)</p> Signup and view all the answers

Qual es le function del cytosol in le production de lactate?

<p>Conversion de glucose a lactate (B)</p> Signup and view all the answers

Qual es le subunitate dehydrogenase de dihydrolipoil?

<p>E3 (B)</p> Signup and view all the answers

Qual es un possibile defecto hereditari del complexo dehydrogenase de piruvato?

<p>Mutacion del subunitate E1 (C)</p> Signup and view all the answers

In le caso reportate, qual es le concentration de lactate in le sanguine del infante de 8 menses?

<p>9 mM (A)</p> Signup and view all the answers

Quod representa un possibile symptomate clinic in babies con defectos in le complexo dehydrogenase de piruvato?

<p>Incapacitate de ganar peso (B)</p> Signup and view all the answers

Qual es le cofactor que lipoic acid require pro functionar efficacemente?

<p>Acido pantotenico (B5) (D)</p> Signup and view all the answers

Quid representa un possibile consequentia del piling de acetyl CoA o acyl CoA pro le cellulas?

<p>Accumulation de toxinas cellular (C)</p> Signup and view all the answers

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