3. Hemophilia.pdf

Hemophilia Pediatrics: Hematological Pathophysiology Hemophilia A Hemophilia is an inherited bleeding disorder in which the blood cannot clot Lack of clotting factor VIII (8) normally....

Hemophilia Pediatrics: Hematological Pathophysiology Hemophilia A Hemophilia is an inherited bleeding disorder in which the blood cannot clot Lack of clotting factor VIII (8) normally. Clients have an increased risk of excessive bleeding from small Hemophilia B injuries like a paper cut or a fall on the ground. Lack of clotting factor IX (9) Clotting factor VIII Clotting factor IX HESI Question A nurse is caring for a patient diagnosed with hemophilia A. The nurse knows this type of hemophilia is caused by an absence of which clotting factor? Hemophilia A Hemophilia B VIII Signs & Symptoms HESI Question A nurse is caring for a patient with hemophilia. Which concerns Pain, Bruising, & Petechiae would be expected on the nursing care plan? Ineffective tissue perfusion Select all that apply. Joint stiffness & Pain Anxiety Lack of mobility Deficit of fluid volume Ineffective tissue perfusion Treatment Kaplan Question Q1 Client with hemophilia develops painful swelling of the knee after bumping the leg... which initial action is most AVOID Injections: IV, IM, SQ appropriate for the nurse to take? Apply ice to the knee and Administers coagulation elevate the leg replacement factors Q2 The nurse reviews the medical record for 4 hr a client diagnosed with hemophilia. It is Ice packs & most important for the nurse to question Meperidine Elevate the affected area which entry? Meperidine 75mg IM q 4 hr for severe pain Education 4 NCLEX TIPS Vaccinations 1. Wear a medical alert bracelet at all times 2 NCLEX TIPS 2. Avoid giving the child 1. Admin vaccines via over-the-counter aspirin subcutaneous route The big bleed risk with the smallest needle 3. Noncontact sports: 5 min swimming, jogging 2. Hold pressure on the injection site for 4. Joint destruction = 5 minutes or more. long-term complication