In terms of disease classification, which description applies to limited cutaneous systemic sclerosis?
Understand the Problem
The question is asking for the correct description that applies to limited cutaneous systemic sclerosis, which is related to disease classification in the context of scleroderma. We need to identify the accurate definition from the provided options, focusing on the distinct characteristics of this disease variant.
Answer
Limited cutaneous systemic sclerosis affects mainly the skin of the fingers, hands, face, and forearms and is associated with Raynaud's phenomenon.
Limited cutaneous systemic sclerosis (lcSSc) is characterized by skin involvement restricted mainly to the fingers, hands, face, and forearms. It is usually associated with Raynaud's phenomenon and may include features such as CREST syndrome.
Answer for screen readers
Limited cutaneous systemic sclerosis (lcSSc) is characterized by skin involvement restricted mainly to the fingers, hands, face, and forearms. It is usually associated with Raynaud's phenomenon and may include features such as CREST syndrome.
More Information
Limited cutaneous systemic sclerosis is a type of systemic sclerosis, also known as scleroderma, where skin thickening is limited but can be associated with more serious systemic effects.
Tips
Confusing limited cutaneous systemic sclerosis with diffuse systemic sclerosis is common. The key difference is that in limited cutaneous systemic sclerosis, skin involvement does not extend beyond the elbows and knees.
Sources
- Limited cutaneous systemic sclerosis - BMJ Best Practice - bestpractice.bmj.com
- Limited cutaneous systemic sclerosis - Orphanet - orpha.net
- Systemic sclerosis - Orphanet - orpha.net
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