40 Questions
What is the primary characteristic of café au lait skin pigmentation in Mc Cune-Albright Syndrome?
It is limited to one side of the body and has irregular margins.
Focal cemento-osseous dysplasia typically occurs in which area of the jaw?
Posterior area of the mandible
What is the most common fibro-osseous lesion in the jaw?
Cemento-osseous dysplasia
What is the endocrine abnormality associated with Mc Cune-Albright Syndrome?
Premature sexual development in girls
What is the typical size of focal cemento-osseous dysplasia?
Less than 1.5 cm in diameter
What is a rare but potential complication of fibrous dysplasia?
Sarcomatous transformation
What is a common oral manifestation of fibrous dysplasia?
Unilateral swelling of the maxilla
When does the mutation of the GNAS1 gene occur in fibrous dysplasia?
During embryonic development
What is a skeletal deformity that can occur in fibrous dysplasia?
Limb length discrepancy
What is the term for fibrous dysplasia that involves multiple bones?
Polyostotic fibrous dysplasia
What is a characteristic of monostotic fibrous dysplasia in terms of skeletal deformities?
Expansion of the buccal and lingual plates of the mandible
What is a potential dental complication of monostotic fibrous dysplasia?
Displacement of teeth due to bone expansion
What is a characteristic of polyostotic fibrous dysplasia in terms of age of diagnosis?
Usually diagnosed before 10 years of age
What is a potential complication of monostotic fibrous dysplasia in terms of sarcomatous transformation?
Malignant transformation into osteosarcoma
What is a laboratory finding associated with monostotic fibrous dysplasia?
Normal serum calcium and alkaline phosphatase levels
What is a cardiovascular complication of Paget's disease of bone due to increased bone vascularity with multiple arterio-venous shunts during active disease?
Heart failure
What is a potential complication of Paget's disease of bone in the maxilla?
Lion-like facial appearance
What is a potential complication of tooth extraction in Paget's disease of bone during the avascular sclerotic phase?
All of the above
What is a potential long-term complication of Paget's disease of bone?
Osteosarcoma
What is a characteristic radiographic feature of Paget's disease of bone?
Mosaic or jigsaw puzzle appearance
What is a characteristic feature of the final radiopaque stage of Cemento-osseous dysplasia?
Individual trabeculae fuse to form a sheet of sclerotic, cemento-osseous material
What is the main concern in managing asymptomatic patients with Cemento-osseous dysplasia?
Maintaining good oral hygiene to avoid periodontal conditions and teeth loss
What is a characteristic feature of Familial gigantiform cementoma?
A rare hereditary disorder characterized by cemento-osseous proliferation
What is Ossifying (cemento-ossifying) Fibroma?
A benign fibro-osseous neoplasm affecting the jaws and craniofacial skeleton
Why are surgical procedures generally avoided in symptomatic patients with Cemento-osseous dysplasia?
Because the lesions are hypovascular and prone to necrosis and secondary infection
What is a possible consequence of Paget's disease of bone in the skull?
Increase in circumference of the head
What is a common dental complication of Paget's disease of bone?
Dentures no longer fit
Which of the following is a radiographic feature of Paget's disease of bone?
Patchy areas of sclerotic bone
What is a possible skeletal deformity resulting from Paget's disease of bone?
Bowing deformity of weight-bearing bones
Which of the following is NOT a clinical feature of Paget's disease of bone?
Fever
What is a potential neurologic complication of Paget's disease of bone?
Deafness
What is the primary laboratory finding in Paget's disease of bone?
High serum alkaline phosphatase levels
What is the hallmark of Paget's disease of bone histopathology?
Mosaic appearance
What is the primary treatment for Paget's disease of bone?
Bisphosphonate therapy
What is a complication of Paget's disease that can occur due to encroachment on foramina?
Headache
What is a potential complication of Paget's disease in the skeletal system?
Sarcomatous transformation
What is the primary goal of bisphosphonate therapy in Paget's disease?
All of the above
What is a characteristic histopathological feature of Paget's disease of bone?
Basophilic reversal lines
What is a common feature of the bone in Paget's disease?
Mosaic appearance
What is a complication of Paget's disease that can occur due to vascular fibrous connective tissue?
Dental complications
This quiz covers the clinical and radiographic features of monostotic fibrous dysplasia, a benign bone lesion that can affect the jawbone. It includes signs and symptoms, such as buccal and palatal enlargement, tooth displacement, and radiographic patterns.
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