Monostotic Fibrous Dysplasia in Dentistry

What is the primary characteristic of café au lait skin pigmentation in Mc Cune-Albright Syndrome?

It is limited to one side of the body and has irregular margins. (correct)
It occurs on both sides of the body and has irregular margins.
It occurs on both sides of the body and has regular margins.
It is limited to one side of the body and has regular margins.

Focal cemento-osseous dysplasia typically occurs in which area of the jaw?

Posterior area of the maxilla
Posterior area of the mandible (correct)
Anterior area of the mandible
Anterior area of the maxilla

What is the most common fibro-osseous lesion in the jaw?

Fibrous dysplasia
Osteosarcoma
Cemento-osseous dysplasia (correct)
Ossifying fibroma

What is the endocrine abnormality associated with Mc Cune-Albright Syndrome?

Premature sexual development in girls (A) Signup and view all the answers

What is the typical size of focal cemento-osseous dysplasia?

Less than 1.5 cm in diameter (D) Signup and view all the answers

What is a rare but potential complication of fibrous dysplasia?

Sarcomatous transformation (B) Signup and view all the answers

What is a common oral manifestation of fibrous dysplasia?

Unilateral swelling of the maxilla (D) Signup and view all the answers

When does the mutation of the GNAS1 gene occur in fibrous dysplasia?

During embryonic development (C) Signup and view all the answers

What is a skeletal deformity that can occur in fibrous dysplasia?

Limb length discrepancy (D) Signup and view all the answers

What is the term for fibrous dysplasia that involves multiple bones?

Polyostotic fibrous dysplasia (A) Signup and view all the answers

What is a characteristic of monostotic fibrous dysplasia in terms of skeletal deformities?

Expansion of the buccal and lingual plates of the mandible (D) Signup and view all the answers

What is a potential dental complication of monostotic fibrous dysplasia?

Displacement of teeth due to bone expansion (A) Signup and view all the answers

What is a characteristic of polyostotic fibrous dysplasia in terms of age of diagnosis?

Usually diagnosed before 10 years of age (C) Signup and view all the answers

What is a potential complication of monostotic fibrous dysplasia in terms of sarcomatous transformation?

Malignant transformation into osteosarcoma (B) Signup and view all the answers

What is a laboratory finding associated with monostotic fibrous dysplasia?

Normal serum calcium and alkaline phosphatase levels (C) Signup and view all the answers

What is a cardiovascular complication of Paget's disease of bone due to increased bone vascularity with multiple arterio-venous shunts during active disease?

Heart failure (A) Signup and view all the answers

What is a potential complication of Paget's disease of bone in the maxilla?

Lion-like facial appearance (A) Signup and view all the answers

What is a potential complication of tooth extraction in Paget's disease of bone during the avascular sclerotic phase?

All of the above (D) Signup and view all the answers

What is a potential long-term complication of Paget's disease of bone?

Osteosarcoma (B) Signup and view all the answers

What is a characteristic radiographic feature of Paget's disease of bone?

Mosaic or jigsaw puzzle appearance (C) Signup and view all the answers

What is a characteristic feature of the final radiopaque stage of Cemento-osseous dysplasia?

Individual trabeculae fuse to form a sheet of sclerotic, cemento-osseous material (A) Signup and view all the answers

What is the main concern in managing asymptomatic patients with Cemento-osseous dysplasia?

Maintaining good oral hygiene to avoid periodontal conditions and teeth loss (A) Signup and view all the answers

What is a characteristic feature of Familial gigantiform cementoma?

A rare hereditary disorder characterized by cemento-osseous proliferation (A) Signup and view all the answers

What is Ossifying (cemento-ossifying) Fibroma?

A benign fibro-osseous neoplasm affecting the jaws and craniofacial skeleton (C) Signup and view all the answers

Why are surgical procedures generally avoided in symptomatic patients with Cemento-osseous dysplasia?

Because the lesions are hypovascular and prone to necrosis and secondary infection (D) Signup and view all the answers

What is a possible consequence of Paget's disease of bone in the skull?

Increase in circumference of the head (A) Signup and view all the answers

What is a common dental complication of Paget's disease of bone?

Dentures no longer fit (C) Signup and view all the answers

Which of the following is a radiographic feature of Paget's disease of bone?

Patchy areas of sclerotic bone (B) Signup and view all the answers

What is a possible skeletal deformity resulting from Paget's disease of bone?

Bowing deformity of weight-bearing bones (D) Signup and view all the answers

Which of the following is NOT a clinical feature of Paget's disease of bone?

Fever (D) Signup and view all the answers

What is a potential neurologic complication of Paget's disease of bone?

Deafness (A) Signup and view all the answers

What is the primary laboratory finding in Paget's disease of bone?

High serum alkaline phosphatase levels (B) Signup and view all the answers

What is the hallmark of Paget's disease of bone histopathology?

Mosaic appearance (C) Signup and view all the answers

What is the primary treatment for Paget's disease of bone?

Bisphosphonate therapy (C) Signup and view all the answers

What is a complication of Paget's disease that can occur due to encroachment on foramina?

Headache (D) Signup and view all the answers

What is a potential complication of Paget's disease in the skeletal system?

Sarcomatous transformation (C) Signup and view all the answers

What is the primary goal of bisphosphonate therapy in Paget's disease?